Rare prostate tumors are most often histological entities which together represent less than 10% of prostate tumors; some forms are even described in a few rare copies.The immunohistochemistry progress allowed to dismember these various tumors and consequently to modify the therapeutic strategies.Our work is a retrospective study of medical files, displayed over a period of 5 years, between 2009 and 2014, concerning 5 cases of rare tumors of prostate, diagnosed, treated and followed at the urology service of the University Hospital Hassan II in Fez.These cases are divided as follows:Malignant tumors: a lymphoma type B; an Adult Primary Prostate Embryonal Rhabdomyosarcoma; a neuroendocrine tumour ; a leiomyosarcoma. Benign tumors: a leiomyoma. It was about 05 patients, whose ages ranged from 35 to 74ans years. Obstructive and irritative syndrome was the mode of revelation in all patients. In terms of paraclinical exploration: biologically PSA was positive in only one case (a neuroendocrine tumour).In the staging radiographic assessment was conducted; TDM and IRM. Transurethral resection of the prostate was performed in all patients; to allowed to establish the diagnosis of certainty of prostate tumors. Histology and immunohistochemistry were used to adjust for possible treatment. The evolution was favorable for 03 patients without local or distant recurrence and 02 patient died. In the light of our 05 observations and a review of literature, we tried to do an update on the different histological types of rare tumors of the kidney to improve their diagnostic and therapeutic management